Atypical Teratoid/Rhabdoid (ATRT) of Infancy and Childhood
This 8 year old boy presented with findings of a mass in the region of the pineal gland. The malignant rhabdoid
cells show eccentric nuclei and prominent nucleoli. In some cases areas of small blue cells resembling primitive
neuroectodermal tumor are seen and differential diagnosis can be difficult. The term rhabdoid tumor was first
applied to a malignant tumor of the kidney, originally called the rhabdomyosarcomatoid variant of Wilms tumor.
Contributed by Dr. Robert Bagdasaryan
1 minute clinical correlation